Leiomyoma Arising From The Rudimentary Uterus

In this article, leiomyoma arising from the uterus remnant in a patient with Mayer–Rokitansky– Kuster–Hauser (MRKH) syndrome is reported. The patient was a 41-year–old woman with pelvic mass and a history of Mullerian agenesis and serum level of CA125 = 45 U/ml who had exploratory laparotomy. A 6×8×4 cm³ solid and firm mass with smooth surface arising from the uterine remnant as myoma was confirmed. Uterine myoma can even occur in rudimentary uterus and it is one of the differential diagnosis for pelvic mass in cases with Mayer-Rokitansky-Kuster-Hauser syndrome.