MRI appearance of a double inlet and double outlet right ventricle with supero-inferior ventricular relationship

This patient was diagnosed with a double inlet and double outlet RV with supero-inferior ventricular relationship, ventricular inversion was diagnosed on the basis of left-handed topology of the RV, and the straddling of the right-sided mitral valve over an anterior VSD, with its tension apparatus extending into the outflow tract of the RV. MRI was found to be superior to color Doppler echocardiography and contrast ventriculography in the segmental analysis leading to a full understanding of this complex case.