Renal angiomyolipoma with liposarcomatous transformation: A case report and review of the literature

Renal angiomyolipoma is generally benign, although an uncommon subtype (epithelioid angiomyolipoma) may behave more aggressively. Sarcomatous transformation of the disease is exceedingly rare. We report the first case of a high grade round cell liposarcoma arising in a renal angiomyolipoma.