Author/Authors :
Beigel، Roy نويسنده The Heart Institute, Cedars Sinai Medical Center, David Geffen School of Medicine, UCLA , , Carlos Tress، Joao نويسنده Hospital Universitario Pedro Ernesto , , Elizabeth Jane Thomson، Louise نويسنده The Heart Institute, Cedars Sinai Medical Center, David Geffen School of Medicine, UCLA , , James Luthringer، Daniel نويسنده Department of Pathology, Cedars Sinai Medical Center, David Geffen School of Medicine , , Shturman، Alexander نويسنده Department of Cardiovascular Medicine, Western Galilee Hospital, Bar Ilan University , , Trento، Alfredo نويسنده The Heart Institute, Cedars Sinai Medical Center, David Geffen School of Medicine, UCLA , , James Siegel، Robert نويسنده The Heart Institute, Cedars Sinai Medical Center, David Geffen School of Medicine, UCLA ,
Abstract :
While primary malignant tumors of the heart are rare, angiosarcomas are the most common cardiac malignant tumors. We describe a 23-year-old woman who presented with a right atrial mass, which was discovered to be a cardiac angiosarcoma. We demonstrate the use of several noninvasive imaging modalities along with pathology confirmation for the definitive and comprehensive diagnosis of a cardiac angiosarcoma, a rare entity by itself. With the increasing availability of noninvasive imaging techniques, the diagnosis of angiosarcomas can be made at earlier stages. If angiosarcomas are left untreated, their prognosis is very poor. Therapeutic options include surgical excision, chemotherapy, radiation therapy, and heart transplantation or a combination of these.