Intermittent Prolapse of Right Atrial Myxoma in a Four-Year-Old Girl

Right atrial myxoma is a rare disease among children and its clinical presentation is not specific. We reported a four-year-old girl with exertional dyspnea in whom investigations revealed a huge right atrial myxoma. The evolution was quite unusual; the girl presented syncope secondary to an intermittent prolapse of the tumor through the tricuspid valve. After complete resection, her symptoms were relieved without any recurrence of the tumor. The authors emphasize on the rarity of this pathology among children, its clinical polymorphism, the necessity of a rapid diagnosis, and an appropriate treatment to avoid complications and recurrence of the tumor.