Author/Authors :
KHOSRAVI، ALIREZA نويسنده , , Behjati، Mohaddeseh نويسنده , , Nilforoush، Peyman نويسنده General Practitioner, Delasa Heart Center, Sina Heart Hospital, Isfahan, Iran , , Saieedi، Mahmoud نويسنده Isfahan Hypertension Research Center, Isfahan Cardiovascular Research Institute, Isfahan University of Medical Sciences, Isfahan, Iran , , Balouchi، Abbas نويسنده Isfahan Hypertension Research Center, Isfahan Cardiovascular Research Institute, Isfahan University of Medical Sciences, Isfahan, Iran ,
Abstract :
BACKGROUND: Although Marfan’s syndrome is a disease with various phenotypes, but the
major mechanism of death is cardiovascular complication. Aortic dissection is a major cause of
death in Marfan syndrome.
CASE REPORT: A 30-year-old man with severe refractory chest and left flank pain and
history of previously surgically repaired Type A aortic dissection was referred to the
hospital. His typical manifestations of Marfan’s syndrome were identified. Cardiovascular
imaging showed an acute spiral dissection in the descending aorta extending to the left renal
and femoral arteries with no evidence of thrombosis in its huge false lumen (8 cm). By the
diagnosis of acute, expanded, spiral, Type B aortic dissection, he underwent the stent
grafting of dissected aorta. He discharged without any complication. On follow-up
cardiovascular imaging, thrombosed false lumen in stented aorta from descending aorta to
the proximal abdominal aorta was seen.
CONCLUSION: Endovascular treatment of Type B dissection is an effective treatment in Type B
dissection, even in patients with Marfan syndrome.
