A Young Boy with Coronary Cameral Fistula

Abstract: Coronary-Cameral Fistula (CCF) is an anomalous connection between a coronary artery and cardiac chamber. Most CCFs are discovered incidentally during angiographic evaluation for coronary vascular disorder. Here, we report a 16-year-old boy with exertional breathlessness for 3 years. There was a continuous murmur at the right para sternal border in the 4th and 5th intercostal space. Echocardiography showed Right Ventricular Hypertrophy (RVH) with strain pattern. Besides, transthoracic echocardiography demonstrated a normally functioning left ventricle, but dilated right atrium and ventricle. The right ventricle also showed hypertrophy and trabeculation. Coronary angiography demonstrated a direct connection between the right ventricular cavity and the right epicardial coronary artery. However, the left coronary arterial system was normal. The patient was treated by ligation of the fistulous connection by off-pump surgery.