Author/Authors :
Farahmand، Fatemeh نويسنده , , Soleimani، Khadije نويسنده Department of Cardiology, Arak University of Medical Sciences, Arak, Iran. Soleimani, Khadije , Hashemi Jazi، Seyed Mojtaba نويسنده Scientific member of Reserch Center of Agriculture Center of Shahrekord , , Shafieyoun، Arezoo نويسنده Research Center for Immunodeficiencies, Childrens Medical Center, Tehran University of Medical Sciences, Tehran, Iran. Shafieyoun, Arezoo , Rezaei، Nima نويسنده , , Yousefi، Azizollah نويسنده Department of Pediatric Gastroenterology, Pediatrics Center of Excellence, Childrens Medical Center,
Tehran University of Medical Sciences, Tehran, Iran. Yousefi, Azizollah
Abstract :
Congenital hepatic fibrosis (CHF) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. Herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (CHF). Prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients.