Author/Authors :
M. ALLMENDINGER، Andrew نويسنده The Department of Radiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, MA, USA , , A. RICCI، Joseph نويسنده The Division of Plastic Surgery, Brigham and Women’s Hospital, Harvard Medical School, Boston, MA, USA , , S. DESAI ، Naman نويسنده The Department of Radiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, MA, USA , , VISWANADHAN، Narayan نويسنده The Department of Radiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, MA, USA , , Rodriguez، Diana Jasso de نويسنده ,
Abstract :
Linear scleroderma “en coup de sabre” is a subset of localized scleroderma
with band-like sclerotic lesions typically involving the fronto-parietal regions
of the scalp. Patients often present with neurologic symptoms. On imaging,
patients may have lesions in the cerebrum ipsilateral to the scalp abnormality.
Infratentorial lesions and other lesions not closely associated with the overlying
scalp abnormality, such as those found in the cerebellum, have been reported,
but are extremely uncommon. We present a case of an 8-year-old boy with a left
fronto-parietal “en coup de sabre” scalp lesion and describe the neuroimaging
findings of a progressively enlarging left cerebellar lesion discovered
incidentally on routine magnetic resonance imaging. Interestingly, the patient
had no neurologic symptoms given the size of the mass identified.
