Author/Authors :
Karami, A Department of Surgery - Department of Pathology - Iranian Hospital - Dubai, UAE , Azizi, S Department of Surgery - Department of Pathology - Iranian Hospital - Dubai, UAE , Payombarnia, A Department of Surgery - Department of Pathology - Iranian Hospital - Dubai, UAE , Rezaee, N Department of Surgery - Department of Pathology - Iranian Hospital - Dubai, UAE , Azarpira, N Department of Pathology - Shiraz University ofMedical Sciences, Shiraz
Abstract :
Leiomyosarcoma of the inferior vena cava (IVC) is a rare sarcoma, but it is the most common primary malignancy
of the IVC. It has an extremely gloomy prognosis. We describe a 40 year-old white female complaining of
abdominal fullness for 7 weeks before she sought medical assistance. Initial work-up including sonography and
computed tomography showed a huge tumoral mass in the abdominal cavity seemingly originating from the IVC
with displacement of the right ureter and hydronephrosis. The patient underwent surgical resection of the tumor.
Pathologic diagnosis was leiomyosarcoma. Postoperatively, she was placed on coumadin and adjuvant chemotherapy
was started. Considering the aggressiveness of this tumor, early radical enblock resection with clear
margins is still the only chance for long-term survival
