Author/Authors :
Bansal, Anand Rai Department of Surgery and Urology - Sharma Postgraduate Institute of Medical Sciences - Rohtak, India , Griwan, Mahavir Singh Department of Surgery and Urology - Sharma Postgraduate Institute of Medical Sciences - Rohtak, India , Karthikeyan, Yayathi Rajan Department of Surgery and Urology - Sharma Postgraduate Institute of Medical Sciences - Rohtak, India , Singh, Santosh Kumar Department of Surgery and Urology - Sharma Postgraduate Institute of Medical Sciences - Rohtak, India
Abstract :
Malignant peripheral nerve-sheath tumor (MPNST) is a high-grade malignant tumor of ecto-mesenchymal origin comprising approximately
10% of soft-tissue sarcomas. They tend to occur associated with neurofibromatosis or sporadically. Here we report a MPNST at an extremely rare
location and behavior causing disappearance of the entire kidney. Patient evaluation included clinical, biochemical and radiological studies
before treatment. Histological study revealed the rare diagnosis. Patient was asymptomatic at six-month follow-up after treatment.