Apert Syndrome: Report of a Case with Emphasis on Oral Manifestations

To report the oral findings, including dental anomalies, ectopic eruption of the maxillarypermanent first molars and periodontal disease and soft tissue alterations, in a subject withApert syndrome. Clinical and radiographic examination of a patient with Apert syndrome,aged 21 years old, not previously submitted for orthodontic or orthognathic treatment.Dental anomalies were present in a patient. Intraoral evaluation revealed poor oral hygienewith varying degrees of periodontal involvement, an arched swelling (pseudo cleft configuration),class III malocclusion, anterior open bite, posterior crossbite, supernumeraryteeth, ectopic eruption and creamy white enamel opacities, an excessively large appearingtongue and a v-shaped maxillary arch. The occurrence of typical lateral palatal swellingsagrees with the literature. The high prevalence of dental anomalies and ectopic eruptionmay suggest a possible etiologic relationship with the syndrome.