Feminizing Adrenal Tumor: A Rare Presentation

Malignant adrenocortical tumor (ACT), a rare entity with an incidence of 1-2/million, is uncommon in pediatric population[1]. These tumors are functional with varied endocrine syndromes, most frequent being rapidly progressing Cushing syndrome with/out virilization. In males estrogen-secreting tumors lead to gynecomastia and are invariably malignant[2]. The modality of treatment is surgical resection of tumor by laparoscopy or open laparotomy followed by chemotherapy in selected cases based on new unio‎n International Contre Cancer (UICC) staging by WHO. Laparoscopic adrenalectomy as safe choice of surgical approach is being extensively described in recent literature. The prognosis depends on the tumor stage and five-year survival in different series ranged between 16 and 38%[2]. We report on a feminizing adrenal tumor in a six year old male child who presented with bilateral gynecomastia for its rarity.