Author/Authors :
Toossi, Parviz Skin Research Center - Department of Dermatology - Shahid Beheshti University of Medical Sciences, Tehran , Hejazi, Somayeh Skin Research Center - Department of Dermatology - Shahid Beheshti University of Medical Sciences, Tehran , Shakoei, Safoura Skin Research Center - Department of Dermatology - Shahid Beheshti University of Medical Sciences, Tehran , Asadi-Kani, Zahra Skin Research Center - Department of Dermatology - Shahid Beheshti University of Medical Sciences, Tehran
Abstract :
Pemphigus vulgaris (PV) is a potentially fatal autoimmune
mucocutaneous blistering disease. Although PV occurs
predominantly in adulthood, in the 3rd to 5th decades of life,
there have rarely been reports of childhood cases which are often
misdiagnosed. It presents as oral blisters that rupture rapidly and
progress to painful erosions. Most patients develop cutaneous
flaccid blisters that rupture easily and leave painful erosions,
which are slow to heal. These erosions are prone to secondary
bacterial infection. Without treatment, the disease is progressive
and the mortality rate is about 100%. We report an 8-year-old
girl who was referred to our clinic from a pediatric center with
mucocutaneous recalcitrant blisters.
