Title of article :
Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Adrenal Gland of a Child
Author/Authors :
Goudarzipour, Kourosh Pediatric Congenital Hematologic Disorders Research Center - Shahid Beheshti University of Medical Science , Farahmandi, Farzaneh Mofid Children’s Hospital - Shahid Beheshti University of Medical Science , Mohammadi, Ahmad Pediatric Congenital Hematologic Disorders Research Center - Shahid Beheshti University of Medical Science , Taherian, Reza student Research Committee - School of Medicine - Shahid Beheshti University of Medical Sciences
Abstract :
Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/PNET) typically occurs in long or flat bones, soft tissues, or less often, solid organs. Ewing sarcoma/peripheral primitive neuroectodermal tumor arising from the adrenal gland is extremely rare, especially in children, and only limited cases are reported previously. Herein, we review a case of a 22-month-old girl who presented to our department with abdominal pain, bulging of the left flank, and a nonfunctioning adrenal lesion which was found to be an adrenal ES/PNET. The patient was successfully treated with surgery and adjuvant chemotherapy. Since delayed diagnosis may result in metastatic lesions, this case underscores the importance of considering ES/PNET in the differential diagnosis of large adrenal masses.
Keywords :
child , Ewing sarcoma/peripheral primitive neuroectodermal tumors , adrenal gland
Journal title :
Astroparticle Physics
