NEVOID BASAL CELL CARCINOMA SYNDROME

A 15-year-old man was referred to our department with multiple lesions on the scalp, neck, abdomen, and back which -were proved to be basal cell carcinomas. The patient had a history of craniotomy at 3 years of age for exision of a cerebellar medulloblastoma, followed by cranioaxis irradiation post-operatively. On physical examination, hypertelorism, broad nose bridge and a slightly bulged out chest cage were noted. Chest X-ray revealed deformity of the chest wall. A diagnosis of nevoid basal cell carcinoma (NBCC) syndrome was made.