Title of article :
Gorham’s Disease of Cervicothoracic Spine
Author/Authors :
Rastegar Khodakaram Bone and Joint Reconstruction Research Center - Shafa Orthopedic Hospital - Iran University of Medical Sciences - Tehran, Iran , Ghandhari Hasan Bone and Joint Reconstruction Research Center - Shafa Orthopedic Hospital - Iran University of Medical Sciences - Tehran, Iran , Ameri Ebrahim Bone and Joint Reconstruction Research Center - Shafa Orthopedic Hospital - Iran University of Medical Sciences - Tehran, Iran , Nikouei Farshad Bone and Joint Reconstruction Research Center - Shafa Orthopedic Hospital - Iran University of Medical Sciences - Tehran, Iran , Shakeri Mohammadreza Bone and Joint Reconstruction Research Center - Shafa Orthopedic Hospital - Iran University of Medical Sciences - Tehran, Iran
Abstract :
Gorham’s disease is a rare enigmatic bone disorder associated with obscure
osteolysis pattern, challenging diagnosis and treatment. Particularly, there is a high level of
controversy regarding the diagnosis and strategy of treatment in the spinal involvement of
Gorham’s disease that is generally presented with a kind of spinal deformity.
Case Presentation: Here, we report a case of Gorham’s disease of the spine manifested with
spinal cord complications and lacking any spinal deformity. The patient was managed through
a two-stage spinal cord decompression technique. The symptoms were resolved afterward and
five-year visits did not demonstrate any significant complication.
Conclusion: This case reveals that the Gorham’s disease of the spine could be presented with
spinal cord complication alone. Accordingly, the strategy of treatment should be established
based on the occurrence of spinal cord complications or magnitude of spinal deformity.
Keywords :
Spinal cord compression , Spine Symptoms , Gorham’s disease
Journal title :
Shafa Orthopedic Journal