An Unusual Type of Choledochal Cyst with Huge Dilation of Extrahepatic Bile Duct from Hilum to Ampulla of Vater; a Case Report and Literature Review

Introduction: Choledochal cyst is a rare problem, defined as congenital dilatation of the biliary tract. There are five particular categories of choledochal cysts with some sub-types. The optimal management is removal of entire extrahepatic biliary system in addition to cholecystectomy and reconstruction by Roux-en-Y hepaticojejunostomy. Case Presentation:We reported a 25 years old patient with a giant choledochal cyst. This Choledochal cystmaybelong to subtype 1a plus affecting the intrapancreatic portion of commonbile duct (CBD). The cyst was successfully resected without any complications. Conclusions: Intraoperative finding of choledochal cyst is very important, therefore, knowledge of potential presence of this rare disease and its management with respect to anatomical variations is very important for surgeons.