Title of article :
Anesthesia for herniotomy in Schwartz–Jampel syndrome
Author/Authors :
Ewees, Bahaa El-Din Ain Shams University - Faculty of Medicine - Department of Anesthesiology, Intensive Care and Pain Management, Egypt , El Fawy, Dalia M. Ain Shams University - Faculty of Medicine - Department of Anesthesiology , Intensive Care and Pain Management, Egypt
Abstract :
Patients with neuromuscular disorders may develop specific anaesthetic complications; these include pulmonary insufficiency, cardiac arrhythmias, thermoregulatory instability and technical difficulties with tracheal intubation. We describe the anaesthetic management of a child with a rare autosomal recessive disorder, Schwartz-Jampel syndrome, characterised by various musculoskeletal disorders and a potential for thermoregulatory dysfunction.
Keywords :
anesthesia , Schwartez , Jampel syndrome
Journal title :
Ain Shams Journal of Anesthesiology(ASJA)
Journal title :
Ain Shams Journal of Anesthesiology(ASJA)
