Author/Authors :
Sadeghpour, Anita tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران , Kyavar, Majid tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران , Yousefnia, Mohammad Ali tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران , Chamanian, Soheila tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران , Khajeali, Zahra tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران , Alizadeh Sani, Zahra tehran university of medical sciences tums - Rajaie Cardiovascular Medical and Research Center - Department of Cardiovascular Medicine, Echocardiography Lab, تهران, ايران
Abstract :
Hypoplastic right ventricle is a rare congenital heart disease, as attested to by the small number of cases reported so far. We present a patient with hypoplastic right ventricle and multiple associated anomalies, namely ventricular septal defect, atrial septal defect, and pulmonary stenosis. Our principal concern was whether biventricular repair or Fontan type surgery would be the optimal management in this patient. We succeeded in performing biventricular repair via multi-modality cardiac imaging using intraoperative transesophageal echocardiography.
