POLYSPLENIA IN ADULT PATIENT WITH WANDERING PELVIC AND TORSION SPLEEN

Aim: To present a rare case of congenital polysplenia in adult patient present with sudden abdominal pain due to twisted wondering spleen in the pelvis. Methods: This is a single case report investigated preoperative and examined clinically where surgical intervention was performed due to rapidly progressive enlarged hypogastric mass. Result: Adult man with polysplenia and minor congenital heart disease presented with twisted accessory spleen wondering in the pelvis with long pedicle. Discussion: Polysplenia syndrome (PSS) is a type of situs ambiguous,usually associated with severe congenital heart diseases and rarely these patient reached adult life. The unique sign of the polysplenia is the presence of multiple spleens, ranging from 2 to 16. We present a case of polysplenia in adult patient with minor heart anomalies and four spleens one of them is very huge and discovered as emergency with torsion wondering pelvic spleen