Successful treatment of electrical storm in a child with early repolarization syndrome with orciprenaline and radiofrequency ablation

Early repolarization (ER) is a benign electrographic pattern and described as J-point elevation ≥1 mm in two or more adjacent inferior and/or lateral derivations, resulting in QRS slurring or notching (1-3). Some researchs have shown that ER might be one of the arrhythmogenic reasons for idiopathic ventricular fibrillation (VF) (1, 3). Here we present the case of a boy with inferolateral ER complicated by an electrical storm and treated with orciprenaline and radiofrequency ablation of the Purkinje network.