Author/Authors :
Taheri, Jamile Bigom shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Azimi, Somayyeh shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Mortazavi, Hamed shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Babaee, Somayyeh shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Tarahhomi, Mohammad-Reza hamadan university of medical sciences - School of Medicine - Department of Plastic Surgery, ايران
Abstract :
Objectives: Ectrodactyly-ectodermal dysplasia-clefting syndrome (EEC) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. This study presents an Iranian case with classic features and oral complications. Case: We report a 20-year old female with all manifestations of this syndrome. The simultaneous presence of these three malformations is extremely rare; the incidence is estimated to be 1.5 per 100.000.000 births. Conclusion: Oral hygiene management of patients with EEC syndrome is important and dental practitioners need to know the oral and dental conditions presenting with this syndrome.
Keywords :
Ectrodactyly , Ectodermal dysplasia , Cleft lip , Oral manifestations , Dental complications.
