Title of article
Kartagener Syndrome With Focal Segmental Glomerulosclerosis
Author/Authors
Momeni, Ali shahrekord university of medical sciences - Division of Nephrology, Department of Internal Medicine, ايران , Doroushi, Behzad shahrekord university of medical sciences - Department of Internal Medicine, Division of Rheumatology, ايران , Taheri, Nadia isfahan university of medical sciences - Department of Pathology, ايران
From page
499
To page
501
Abstract
Primary ciliary dyskinesia is characterized by congenital impairment of mucociliary clearance. Kartagener syndrome (KS) is a clinical variant of primary ciliary dyskinesia which is involved in situs inversus associated with chronic respiratory infections. In addition, glomerular disease in KS syndrome is rare and reported cases are limited. We had a 27-year-old female patient with KS who presented with proteinuria, hematuria, normal kidney function, and a family history of systemic lupus erythematosus. Kidney biopsy showed segmental scar with adhesion to Bowman capsule, which was indicative of focal segmental glomerulosclerosis.
Keywords
Kartagener syndrome , focal segmental glomerulosclerosis , hematuria
Journal title
Iranian Journal of Kidney Diseases (IJKD)
Journal title
Iranian Journal of Kidney Diseases (IJKD)
Record number
2590229
Link To Document