Author/Authors :
Biçer, Cihangir Erciyes University - Faculty of Medicine - Department of Anaesthesiology and Reanimation, Turkey , Eskitasçioglu, Teoman Erciyes University - Department of PLastic Surgery and Reconstruction, Turkey , Aksu, Recep Erciyes University - Faculty of Medicine - Department of Anesthesiology and Reanimation, Turkey , Madenoglu, Halit Erciyes University - Faculty of Medicine - Department of Anesthesiology and Reanimation, Turkey
Abstract :
The Beckwith-Wiedemann syndrome is characterized by macroglossia; pre- or postnatal gigantism; abdominal wall defects; hypoglycaemia; umbilical hernia or diastasis recti; ear creases or posterior helical ear pits; facial nevus flammeus; renal anomalies; neoplasms; hemihypertrophy; congenital cardiac malformations; intestinal malrotation; mental retardation; polydactyly; and cleft palate. Anesthetic considerations of 7 months old girl with Beckwith- Wiedemann syndrome during reduction of macroglossia are presented and discussed.
Keywords :
Anesthesia , Beckwith , Wiedemann syndrome , Macroglossia
