Author/Authors :
Morgenstern-Kaplan, Dan Centro de Investigación en Ciencias de la Salud (CICSA) - Facultad de Ciencias de la Salud - Universidad Anáhuac MexicoCampus Norte - Huixquilucan - Edo. de Mexico, Mexico , Blachman-Braun, Ruben Centro de Investigación en Ciencias de la Salud (CICSA) - Facultad de Ciencias de la Salud - Universidad Anáhuac MexicoCampus Norte - Huixquilucan - Edo. de Mexico, Mexico , Aboitiz-Rivera, Carlos Manuel Echocardiography and Hemodynamics Service - Instituto Nacional de Enfermedades Respiratorias - Tlalpan - Mexico City, Mexico , Sarabia-Ortega, Benito Echocardiography and Hemodynamics Service - Instituto Nacional de Enfermedades Respiratorias - Tlalpan - Mexico City, Mexico , Baltazares-Lipp, Mario Enrique Echocardiography and Hemodynamics Service - Instituto Nacional de Enfermedades Respiratorias - Tlalpan - Mexico City, Mexico , Vázquez-Manríquez, María Eugenia Department of Pathology - Instituto Nacional de Enfermedades Respiratorias - Tlalpan, Mexico City, Mexico
Abstract :
Cardiac angiosarcoma is a rare and clinically challenging pathology.It is a high-grade primary malignant tumor of the heart tissue thathas many variants, of which the epithelioid variant is rarely present in the heart or the great vessels. As with many other cardiac tumors,it is mainly a diagnosis of exclusion and the initial diagnostic testis an echocardiogram followed by a biopsy with immunohistochemistryanalysis to ascertain the type of tumor. The differential diagnosis of cardiac tumors is challenging due to the overlapping clinicalmanifestations with different cardiac tumors and systemic diseases. Cardiac angiosarcomas are often aggressive with a poorprognosis even with treatment. Herein, we present a case of the epithelioid variant of a cardiac angiosarcoma in addition to athorough review of the recent literature on the clinical manifestation, diagnosis, and treatment of this type of tumors.