Author/Authors :
De Guido, Claudia Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Calderaro, Adriana Department of Medicine and Surgery - University of Parma, Parma, Italy , Beatrice Ruozi, Maria Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Maffini, Valentina Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Varini, Margherita Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Lapetina, Irene Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Rubini, Monica Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy , Montecchini, Sara Department of Medicine and Surgery - University of Parma, Parma, Italy , Caffarelli, Carlo Department of Medicine and Surgery - Children Hospital “P. Barilla” - University of Parma, Parma, Italy , Dodi, Icilio Children Hospital “P. Barilla” - Azienda Ospedaliero-Universitaria - Parma University Hospital, Parma, Italy
Abstract :
SJS is a rare mucocutaneous syndrome characterized by skin and mucous detachment. The main etiological factors are drugs and infections; sometimes the cause remains unknown. In the prodromal phase we observed non-specific symptoms, followed by mucocutaneous manifestation. Due to risk of complications and mortality a multidisciplinary approach is needed. We present a case of a girl with an atypical presentation of SJS related to Enterovirus. (www.actabiomedica.it)
Keywords :
Steven-Johnson Syndrome , allergy , enterovirus , corticosteroids , cyclosporine A