Title of article
Pulmonary alveolar proteinosis in children: a case series
Author/Authors
Tabatabaei, Ahmad shahid beheshti university of medical sciences - Mofid Children Hospital, تهران, ايران , Karimi, Abdollah shahid beheshti university of medical sciences - Mofid Children Hospital - Pediatric Infectious Research Center, تهران, ايران , Rafiee Tabatabaei, Sedigheh shahid beheshti university of medical sciences - Mofid Children Hospital - Pediatric Infectious Research Center, تهران, ايران , Radpay, Badiozzaman shahid beheshti university of medical sciences - Masih Daneshvari Hospital, تهران, ايران , Jadali, Farzaneh shahid beheshti university of medical sciences - Mofid Children Hospital - Pediatric Infections Research Center, تهران, ايران , Shiva, Farideh shahid beheshti university of medical sciences - Mofid Children Hospital - Pediatric Infectious Research Center, تهران, ايران , Hadipour Jahromy, Mana shahid beheshti university - Pediatric Infections Research Center, تهران, ايران
Pages
5
From page
120
To page
124
Abstract
Pulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is fulminant and fatal, and a late-onset PAP which is similar to the adult form and less severe. Eight children with late-onset PAP were hospitalized from 1998 to 2005 in Mofid Children Hospital. Characteristics of these patients and the methods of diagnosis and treatment are presented in this case series.
Keywords
Pulmonary Alveolar Proteinosis , Respiratory Failure , Respiratory Distress , Children
Journal title
Journal of Research in Medical Sciences
Serial Year
2010
Journal title
Journal of Research in Medical Sciences
Record number
2626379
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