Paget’s disease in an Asian woman

Extramammary Paget s disease is a rare disease, which mainly occurs in postmenopausal women. The case of Paget s disease of vulva, in a 40 year old Asian woman, who presented with a history of intense itching in vulva for 1 year is being reported. After being medically treated, she was diagnosed on Vulval biopsy. Local excision of the vulval lesion was performed, and histopathology revealed Paget s disease, extending close to the surgical margins.Therefore, a re-excision was performed and patient remained disease free at six months follow up.