Author/Authors :
Badar, Quratulain Aga Khan University Hospital - Department of Radiation Oncology, Pakistan , Ali, Nasir Aga Khan University Hospital - Department of Radiation Oncology, Pakistan , Abbasi, Nadeem Aga Khan University Hospital - Department of Radiation Oncology, Pakistan , Ashraf, Shamvil Children Cancer Hospital, Pakistan , Karsan, Farrok Aga Khan University Hospital - Department of Radiation Oncology, Pakistan , Hashmi, Raheel Aga Khan University Hospital - Department of Radiation Oncology, Pakistan
Abstract :
Ewing s sarcoma is the second most common primary tumour of bone in childhood. Less frequently it occurs in soft tissues. Ewing s sarcoma/primitive neuroectodermal tumour (ES/PNET) is an extra ordinarily rare primary tumour in the kidney. Only very few cases of primary renal Ewing s sarcoma have been reported in the literature to date.We present a case of primary right renal Ewing s sarcoma in a 13 year old girl who was diagnosed as a case of stage IV ES/PNET of kidney with metastases to lung and liver. Right nephrectomy was done followed by adjuvant radiotherapy and chemotherapy with complete response to local and distant area.
