Author/Authors :
Yenigun, Ezgi Coskun Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Dede, Fatih Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Ozkayar, Nihal Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Turgut, Didem Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Piskinpasa, Serhan Vahit Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Ozturk, Ramazan Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Koc, Eyup Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey , Odabas, Ali Riza Ankara Numune Research and Education Hospital - Department of Nephrology, Turkey
Abstract :
Autosomal dominant polycystic kidney disease (ADPKD) is an inherited disorder characterized by the development and growth of cysts in the kidneys. Non-nephritic-range proteinuria is a common presentation in ADPKD patients; however, nephrotic syndrome is a rare coincidence. A 52-year-old man is described who was diagnosed with secondary amyloidosis with ADPKD. To our knowledge, this is the first case of amyloidosis associated with frequently infected renal cysts. Patients with ADPKD who show massive proteinuria should be investigated in terms of concomitant glomerular disease.
Keywords :
amyloidosis , nephrotic syndrome , polycystic kidney disease , proteinuria
