Author/Authors :
Nair, Prasad Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait , Al-Otaibi, Torki Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait , Nampoory, Narayanan Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait , Al-Qabandi, Wafa’a Kuwait University - Faculty of Medicine - Department of Pediatrics, Kuwait , Said, Tarek Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait , Abdul Halim, Medhat Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait , Gheith, Osama Hamed Al Essa Organ Transplant Center - Department of Nephrology, Kuwait
Abstract :
Primary hyperoxaluria type-1 (PH-1) is a rare autosomal recessive metabolic disorder leading to excessive oxalate production,deposition of calcium oxalate crystals in the kidney, nephrocalcinosis, progressive renal failure and systemic deposition of oxalate (oxalosis). Combined liver and kidney transplantation (LKT),which has been accepted as the treatment of choice for PH-1, has considerably improved patient and graft survival. Herein,we report our experience of three children with PH-1 who underwent combined LKT,with a review of the literature.
