Case Reports: A 13-year-old boy with a short QT interval

Short QT interval syndrome (SQTS) is a familial clinical-electrocardiographic disorder that was first described by Gussak et al. (1) in 2000. A definitive link between SQTS and familial SCS was described by Gaita et al. (2) in 2003. The electrocardiogram (ECG) is characterized by an abnormally short QT interval, typically less than 320 ms with tallpeaked, narrow, symmetrical T waves. The diagnosis of SQTS can be made when the characteristic ECG findings are present, and it should be suspected in the presence of a family history of SCD, unexplained syncope or ventricular fibrillation. We report a case with a very short QT interval (300 ms) without any history of major cardiac events.