Title of article
Aneurysm of ascending and descending aorta in a 10-year-old-boy with Wiskott-Aldrich syndrome
Author/Authors
Babaoğlu, Kadir Kocaeli University - Faculty of Medicine - Department of Pediatric Cardiology, Turkey , Uyan, Zeynep Seda Kocaeli University - Faculty of Medicine - Department of Pediatric Cardiology, Turkey , Binnetoğlu, Köksal Kocaeli University - Faculty of Medicine - Department of Pediatric Cardiology, Turkey , Yıldız, Cenk Eray Istanbul University - Institute of Cardiology - Department of Cardiovascular Surgery, Turkey , Sarper, Nazan Kocaeli University - Faculty of Medicine - Department of Pediatric Hematology, Turkey
From page
76
To page
77
Abstract
Wiskott- Aldrich Syndrome (WAS) is a recessive genetic disorder linked to the X-chromosome characterized by immune deficiency, eczema and thrombocytopenia. To the best of our knowledge, a few cases of vasculitis or aneurysmal formation have been reported in this syndrome, but the association has not been well established. We report a patient with WAS and extensive aortitis causing severe aneurysmal dilatation in the everywhere of the aorta who underwent successful first stage operation involving replacement of ascending aorta.
Journal title
The Anatolian Journal of Cardiology: Andolu Kardiyoloji Dergisi
Journal title
The Anatolian Journal of Cardiology: Andolu Kardiyoloji Dergisi
Record number
2692481
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