Author/Authors :
Ergül, Yakup Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Center and Research Hospital - Department of Pediatric Cardiology, Turkey , Özyılmaz, İsa Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Center and Research Hospital - Department of Pediatric Cardiology, Turkey , Onan, Sertaç Hanedan Bağcılar Training and Research Hospital - Department of Pediatric Cardiology, Turkey , Güzeltaş, Alper Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Center and Research Hospital - Department of Pediatric Cardiology, Turkey
Abstract :
Short QT syndrome (SQTS) is a cardiac channelopathy associated with sudden cardiac death (SCD) and disposition to atrial-ventricular fibrillation (A-VF). An accelerated ventricular repolarization (VR) abnormality develops in the heart due to an electrical stability disorder secondary to increased extracellular potassium flow in the heart.Therefore, ventricular arrhythmias develop, which cause syncope, convulsion, and SD.
