Author/Authors :
Begic, Edin Department of Cardiology - General Hospital «Prim.dr. Abdulah Nakas», Sarajevo, Bosnia and Herzegovina , Hodzic, Enisa Intensive Care Unit - Clinic for Heart Blood Vessel and Rheumatic Diseases - Clinical Center University of Sarajevo, Sarajevo, Bosnia and Herzegovina , Begic, Zijo Department of Cardiology - Paediatric Clinic - Clinical Center University of Sarajevo, Sarajevo, Bosnia and Herzegovina , Iglica, Amer Intensive Care Unit - Clinic for Heart Blood Vessel and Rheumatic Diseases - Clinical Center University of Sarajevo, Sarajevo, Bosnia and Herzegovina , Begic, Nedim Department of Cardiology - Paediatric Clinic - Clinical Center University of Sarajevo, Sarajevo, Bosnia and Herzegovina , Jusic, Omer Intensive Care Unit - Clinic for Heart Blood Vessel and Rheumatic Diseases - Clinical Center University of Sarajevo, Sarajevo, Bosnia and Herzegovina
Abstract :
Long QT syndrome (LQTS) is a rare (1:2500–1:10,000) inherited disorder characterized by the onset of arrhythmogenic syncope, polymorphic
ventricular tachycardia, and sudden cardiac death. The aim of this article was to describe an unexpected success with an unusual therapeutic
modality of a patient diagnosed with LQTS syndrome (suspected Romano–Ward syndrome) during an 8‑year period. A 59‑year‑old female
patient was admitted to the hospital due to chest pain and nausea, and after diagnostic and therapeutical approach, a permanent dual‑chamber
rate‑modulated (DDDR) pacemaker was implanted instead of the implantable cardioverter defibrillator (ICD). During the 8‑year period,
the patient remained stable, without rhythm disorder. Romano–Ward syndrome as a congenital LQTS carries a high risk of sudden cardiac
death and presents an indication for ICD. In this patient, for objective reasons, this could not be performed. Implantation of a DDDR with an
appropriate pharmacological therapy, including propranolol, in this case, proved to be a successful therapeutic modality.
