Author/Authors :
hinojosa, tiffany university of monterrey - faculty of medicine, San Pedro Garza García, Mexico , ramos, elmira universidad auto´noma de tamaulipas, Tamps, Mexico , lewis, daniel j. baylor college of medicine - school of medicine, Houston, USA , lewis, daniel j. university of texas - md anderson cancer center - department of dermatology, Houston, USA , angel, laurent del universidad auto´noma de tamaulipas, Tamps, Mexico , vangipuram, ramya center for clinical studies, Houston, USA , peranteau, andrew j. center for clinical studies, Houston, USA , tyring, stephen k. center for clinical studies, Houston, USA , tyring, stephen k. university of texas - health science center at houston - department of dermatology, Houston, USA
Abstract :
Rosai-Dorfman disease is a benign, self-limited non-Langerhans cell histiocytosis of unknown etiology. Its most common clinical feature is extraordinary massive painless cervical lymphadenopathy. This entity may be limited to the lymph nodes; however, more than 40% of patients have extranodal involvement, with the skin being the most frequently affected site. Cutaneous disease without the presence of lymphadenopathy is extremely rare but has been reported. We report the intriguing case of exclusively cutaneous Rosai-Dorfman disease in an 80-year-old African-American woman.
Keywords :
Rosai , Dorfman disease , Histiocytosis , Lymphadenopathy , Dermatopathology
