Interruption of aortic arch associated with pulmonary valve stenosis

A newborn male is described who presented with interruption of aortic arch associated with ventricular septal defect and pulmonary valve stenosis. He underwent total corrective surgery and was discharged with good clinical results. The combination of significant right ventricular outflow obstruction and interruption of aortic arch is incompatible with fetal survival unless there are large collateral arteries which arise early in pregnancy. This is the first report of this combination of lesions.