Author/Authors :
Gelincik, İ Erzurum Bölge Eğitim ve Araştırma Hastanesi - Patoloji Kliniği, Turkey , Tok, A Erzurum Bölge Eğitim ve Araştırma Hastanesi - Üroloji Kliniği, Turkey
Abstract :
Renal leiomyosarcomas are very rare and only account for 1-3% of primary renal malignancies. The prognosis for a renal sarcoma is poor, and differentiation from sarcomatoid renal cell carcinoma and a renal sarcoma is particularly necessary. The patient s clinical presentation and imaging findings are not helpful for accurate preoperative diagnosis. The primary treatment is radical nephrectomy with or without adjuvant radiotherapy chemotherapy. The prognosis is poor. We report a case of primary renal leiomyosarcoma of which pathological diagnosis was confirmed immunohistochemically.