AYDOĞAN, Mehmet Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey , GÜNDOĞAN, Alper Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey , TURHAN, Ufuk Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey , UÇAR, Ergün Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey , TOZKOPARAN, Ergun Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey , BİLGİÇ, Hayati Gülhane Askeri Tıp Akademisi - Göğüs Hastalıkları Anabilim Dalı, Turkey

Unilateral pulmonary artery agenesis (case report)

20208

Unilateral pulmonary artery agenesis (UPA) is an uncommon congenital anomaly that results from the absence of ipsilateral sixth aortic arch development. Genetic and mechanical factors have been blamed so far; however, no significant etiological factor has been found up to now. UPA is mostly asymptomatic in adulthood, on the other hand, because of being associated with other congenital cardiac malformations, it is usually symptomatic in childhood. Therefore, the majority of adult patients are identified incidentally with PA chest radiographs performed for different reasons. Typical chest radiographic findings are ipsilateral volume loss, absence of hilar shadow, hemidiaphragm elevation, mediastinal displacement and hyperinflation of thecontrolateral lung. In symptomatic cases, the most frequent symptoms are recurrent pulmonary infections, dyspnea and exercise intolerance. In this article, because of its clinical importance, we report the case of a 16-yearold male who was diagnosed with right pulmonary artery agenesis with typical imaging findings.

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Bronchoscopy , congenital abnormalities , pulmonary artery , pulmonary artery agenesis

Gulhane Medical Journal

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