Author/Authors :
Çetin, Mecnun Celal Bayar Üniversitesi - Tıp Fakültesi - Çocuk Kardiyoloji BD, Turkey , Yıldırımer, Münevver Celal Bayar Üniversitesi - Tıp Fakültesi - Çocuk Kardiyoloji BD, Turkey , Kurdal, Adnan Taner Celal Bayar Üniversitesi - Tıp Fakültesi - Kalp Damar Cerrahisi AD, Turkey , Coşkun, Şenol Celal Bayar Üniversitesi - Tıp Fakültesi - Çocuk Kardiyoloji BD, Turkey
Abstract :
Myocardial noncompaction is a rare type of congenital cardiomyopathy, characterized by trabecular network and deep trabecular recesses located in one or more ventricular segments. Patients generally present with cardiac failure, ventricular arrhythmias, and signs and symptoms related to systemic embolies. We presented two cases of myocardial noncompaction, one with left ventricular involvement and dysfunction, and the other with biventricular involvement and trabecular structures, causing right ventricular outflow tract stenosis which required surgical correction. These cases are remarkable as they had atypical clinical picture including presentation findings and treatment protocols.