Author/Authors :
tricard, t. hôpitaux civil de colmar - department of urology, Colmar, France , lopez, s. hôpitaux civil de colmar - department of urology, Colmar, France , lindner, v. hôpital de hautepierre - department of pathology, Strasbourg, France , jung, j.-l. hôpitaux civil de colmar - department of urology, Colmar, France
Abstract :
Introduction: Perivascular epithelioid cell tumors (PEComas) of the bladder are infrequent localisation of this mesenchymal cancer with uncertain malignant behavior. Case report: We report the case of a 74 years old women who was diagnosed a malignant PEComa of the bladder. She necessited radical cystectomy with orthotopic ileocaecal pouch reconstruction. Histology and immunohistochemistry confirmed the diagnosis of a malignant PEComa of the bladder. We evaluate the literature cases to adjust the prognosis criteria. Conclusion: Evolution and prognosis evaluation remain hard and could necessitate a radical surgery. Prognosis criteria for the bladder PEComas have to be clarified.
NaturalLanguageKeyword :
Bladder , PEComas , Perivascular epithelioid cell sarcoma , Malignant , Cystectomy
