Author/Authors :
Yılmaz, Güliz Celal Bayar University - School of Medicine - Department of Radiology, Turkey , Başara, Işıl Celal Bayar University - School of Medicine - Department of Radiology, Turkey , Ovalı, Gülgün Yılmaz Celal Bayar University - School of Medicine - Department of Radiology, Turkey , Tarhan, Serdar Celal Bayar University - School of Medicine - Department of Radiology, Turkey , Pabuşcu, Yüksel Celal Bayar University - School of Medicine - Department of Radiology, Turkey , Mavioğlu, Hatice Celal Bayar University - School of Medicine - Department of Neurology, Turkey
Abstract :
Susac syndrome is a rare disease of unknown pathogenesis. It is caused by a microangiopathy affecting the arterioles of the brain, retina, and cochlea, giving the classic clinical triad of subacute encephalopathy, visual loss secondary to retinal branch occlusions, and sensorineural hearing loss. Magnetic resonanace imaging, retinal fluorescein angiography, and audiography findings enable diagnosis. Early therapy may reduce sequelae and improve recovery. Herein we report a case of Susac syndrome with all the findings of the disease.