كارديوميوپاتي تحديدي ، آميلوييدوزيس

RIMARY SYSTEMIC AMYLOIDOSIS WITH RCM PRESENTATION OF A CLINICAL CASE

Background & Aim: RCM due to primary systemic amyloidosis is a rare case (Particularly rarity of the diagnosis in vivo). Prognosis of the patient is poor and routine management is not effective. I observe only two male patients with documented diagnosis of the RCM during recent seven years in spite continuous clinical work, and only the present case had a systemic amyloidosis as the etiology of RCM. Case report: This patient was a 31 years old man with complain of fullness sensation at the RUQ of abdomen and dyspnaea is presented from 8 months before his death. The results of the complete evaluation of the patient by the invasive and non-invasive methods showed RCM Needle biopsy of liver and bone marrow showed amyloidal fibrils. The patient was expired because severe heart failure and liver dysfunction eventually. Discussion: Case reports of the RCM are to systemic amyloidosis with specific characters are recorded from the different countries. This disease isn ʹt curable approximately and its predisposing factors are unknown. Deliberative problem of the patient is a prolonged history of nandrolon injection and intake of proteinous drugs. He was a professional athlete (body building).