انسفالوپاتي ميوكلونيك

Myoclonic encephalopathy

Background: The dancing eye syndrome or Opsoclonus- myoclonus syndrome is so called because of the bizarre eye movements which are almost invariably present in this rare condition. They are jerky and correspond with jerky movements of the limbs particularly the arms. The cause of entity is not known with certainty but it is thought to be an autoimmune condition. In approximately 10 percent of cases the condition develops as complication of neuroblastoma. Case report: In this paper we introduce an 18-month old girl. A previously well child becomes irritable and unsteady, had coordinated jerks of arms and legs, and abnormal eye movements. Urine VMA, CSF analysis and EEG were normal. The final diagnosis was Opsoclonus-myoclonus syndrome and the patient was treated with prednisolon and IVIg.