گزارش يك مورد فيستول مادرزادي برونكوازوفاژيال

Congenital Broncho-Esophageal Fistula: A Case Report

Background and Objectives: Bronchopulmonary foregut malformations are a group of rare congenital anomalies affecting the respiratory and upper gastro-intestinal tract. Congenital Broncho-esophageal fistula (BEF) if not associated with esophageal atresia is a rare anomaly. Further BEF in which the right main stem bronchus originates from the esophagus with lung hypoplasia is a very rare anomaly. Only 12 cases have been reported up to date. Case Report: The patient, a 3-month-old infant, was admitted with cough, wheezing, tachypena and FTT. Chest X-ray revealed right lung aplasia. Chest CT scan demonstrated lung hypoplasia. Perfusion scan demonstrated negligible function on the right lung. Rigid bronchoscopy showed absence of right main bronchus. An upper GI contrast study demonstrated a right bronchoesophageal fistula. Right posterolateral thoracotomy was discovered as the right main bronchus originating from the lower third of the esophagus communicated with a hypoplastic of the right lung. The right lung was removed and fistula was ligated. Conclusion: In patients with pulmonary aplasia in eXR, we should rollout broncho-esophageal fistula after pulmonary CTscan with esophagography.