Author/Authors :
Nickavar، Azar نويسنده , , Atefi، Najmessadat نويسنده Department of Dermatology, Aliasghar Childrens Hospital, Iran University of Medical Sciences, Tehran, Iran. Atefi, Najmessadat , Kamyab Hesari، Kambiz نويسنده Dept. of Dermatopathology, Razi Skin Hospital, Tehran University of Medical Sciences, Tehran ,
Abstract :
Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilmsʹ tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.
