Title of article :
Idiopathic Subglottic Stenosis in a Patient with Generalized Port-Wine Stain: A Case Report and Review of Literature
Author/Authors :
Behrangi, Elham Dermatology Department - Rasoul Akram Hospital - Iran University of Medical Sciences, Tehran , Yousefian, Laya Otolaryngology Department - Rasoul Akram Hospital - Iran University of Medical Sciences, Tehran , Moodi, Aliakbar Ziaiyan Hospital - Tehran University of Medical Sciences , Azizian, Zahra Dermatology Department - Rasoul Akram Hospital - Iran University of Medical Sciences, Tehran
Abstract :
Background: Subglottic stenosis is defined as inflammatory narrowing of the airway. It can be related to trauma, intubation, autoimmune disorders, vascular malformations, infection and congenital abnormalities. Pot-Wine Stain (PWS) is a small dermis venous malformation which is present at birth. PWS is found on face and neck, but can occur in throat and can cause subglottic stenosis. Case Report: Authors describe an 18-year-old girl with progressive dyspnea misdiagnosed with asthma having no response to medication. She has no histories of trauma, intubation, gastro-esophageal reflux disease (GERD) or allergy symptoms. Conclusion: Evaluations revealed subglottic stenosis in association with generalized PWS. To the best of our knowledge, this finding has not been reported in English medical literature.
Keywords :
Port-Wine Stain , PWS , Subglottic Stenosis , Vascular Malformation
Journal title :
Astroparticle Physics
