Author/Authors :
YILMAZ, Fatih Akdeniz Üniversitesi - Tıp Fakültesi - Nefroloji Bilim Dalı, Türkiye , AYER, Mesut Haseki Eğitim Ve Araştırma Hastanesi - İç Hastalıkları Kliniği, Türkiye , İNCE, İdris Antalya Eğitim Ve Araştırma Hastanesi - Hematoloji Kliniği, Türkiye , AYER, F. Aylin Haseki Eğitim Ve Araştırma Hastanesi - İç Hastalıkları Kliniği, Türkiye
Abstract :
Paroxysmal nocturnal haemoglobinuria (PNH, Strübing–Marchiafava–Micheli syndrome) is a rare acquired clonal disorder of haematopoietic stem cells causing intravascular haemolysis, haemoglobinuria and occasionally severe venous thrombotic complications. The most important complications of PNH, are thrombotic events, especially affecting intra-abdominal veins. Hepatic vein thrombosis (Budd-Chiari syndrome) is common in PNH patients. Herein, we present a case who was admitted to our clinic with bicytopenia, splenomegaly and diagnosed to have PNH during hospitalization.
